Auteurs: Dhekra Jlassi, Ghada Bouslama, Nour Saida Ben Messaoud, Aya Mtiri, Souha Ben Youssef
Abstract:
Melanotic neuroectodermal tumour of infancy (MNTI) is a rare neoplasm derived from neural crest cells. Although it is fundamentally benign, the tumour may present a locally aggressive behaviour, characterised by a rapid progression and a destructive invasion of adjacent structures, hence causing deformities. It primarily affects the maxilla of infants during the first year of life. Surgical excision is considered as the treatment of choice. The recurrence rate varies between 10% and 15%, and malignant behaviour has been reported in 6.5% of cases. We report
a case of MNTI in 7-month-old male child. We discuss the clinical, radiographic and histologic features of this rare tumour, as well as its surgical management and the follow-up.